A rare case of operated OHVIRA syndrome with a pseudocyst

V.V. Mishra, S.B. Solanki, A. Shajan, R. Aggarwal

Rezumat: Obstructed hemivagina with ipsilateral renal agenesis (OHVIRA) syndrome – also known as Herlyn-Werner-Wunderlich syndrome – is a rare Müllerian anomaly. It was described first in 1992 by Wilson. Uterine anomalies can range from mild segmental abnormalities to unicornuate, bicornuate, didelphic uterus and even the absence of uterus and vagina. Among the most common renal anomalies, there are renal agenesis, renal ectopy, multicystic dysplastic kidney and renal duplication. We present the case of a 26-year-old nulligravida with OHVIRA syndrome, previously operated for rudimentary horn excision, diagnosed with vaginal pseudocyst.
Cuvinte cheie: OHVIRA syndrome, pseudocyst, rare uterine anomaly.